Aneurismas pulmonares associados a trombose na doença de Behçet: um relato de caso
DOI:
https://doi.org/10.47456/rbps.v26isupl_1.44394Keywords:
Doença de Behçet, Aneurisma de artéria pulmonar, Trombose artéria pulmonarAbstract
caracterizada por crises recorrentes de úlceras orais e genitais, além de envolvimento cutâneo, oftálmico, do sistema nervoso central, gastrointestinal e vascular. Outras manifestações podem ocorrer mais raramente, como aneurisma de artéria pulmonar e trombose em artéria pulmonar. Relato de Caso: Relatamos o caso de uma mulher que apresentou dispneia e hemoptise secundárias a aneurismas de artéria pulmonar e trombose na artéria pulmonar causado pela doença de Behçet como primeiras manifestações clínicas. Conclusão: A anticoagulação na trombose pulmonar, sem o uso de imunossupressores em pacientes com doença de Behçet, pode levar a um desfecho desfavorável, pois a vasculite subjacente não será tratada. A suspeita clínica desta condição tem implicações prognósticas, especialmente nas apresentações atípicas, enfatizando a relevância do tema exemplificado neste relato de caso.
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