Pulmonary aneurysms associated with thrombosis in Behçet’s disease: a case report

Renato Lucindo Bolelli de Oliveira; Ruben  Horst Duque; Isac  Ribeiro Moulaz; Anna Carolina Simões Moulin; Rafael Burgomeister Lourenço; Bruna Costa da Mata Moura; Ketty Lysie Libardi Lira Machado

doi:10.47456/rbps.v26isupl_1.44394

Autores

Renato Lucindo Bolelli de Oliveira
Ruben Horst Duque
Isac Ribeiro Moulaz
Anna Carolina Simões Moulin
Rafael Burgomeister Lourenço
Bruna Costa da Mata Moura
Ketty Lysie Libardi Lira Machado

DOI:

https://doi.org/10.47456/rbps.v26isupl_1.44394

Palavras-chave:

Behçet’s disease, Pulmonary artery aneurysm, pulmonary artery thrombosis

Resumo

Introduction: Behçet’s disease is a chronic, multisystemic, inflammatory syndrome characterized by recurrent attacks of oral and genital ulcers, in addition to cutaneous, ophthalmic, central nervous system, gastrointestinal and vascular involvement. Other manifestations may occur more rarely, such as pulmonary artery aneurysm and pulmonary artery thrombosis. Case report: We report a case of a woman presenting with dyspnea and hemoptysis secondary to pulmonary artery aneurysms and pulmonary artery thrombosis caused by Behçet’s disease as the first clinical manifestations. Conclusion: Anticoagulation in thrombosis, without the use of immunosuppressants in patients with Behçet’s Disease, may lead to a poor outcome, as the underlying vasculitis will not be treated. The clinical suspicion of this condition has prognostic implications, especially in atypical presentations, emphasizing the relevance of the theme exemplified in this case report.

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