Relato de casos de Escleredema de Buschke associados à gamopatia monoclonal e à diabetes mellitus tipo 2

Alexandre Calegari Oliosi; Lucia Martins Diniz; Emilly Neves Souza; Luana Amaral de Moura; Marcela  Scárdua Sabbagh de Azevedo

doi:10.47456/rbps.v25i2.41037

Authors

Alexandre Calegari Oliosi Hospital Universitário Cassiano Antonio Moraes - Hucam/Ufes https://orcid.org/0000-0001-6191-631X
Lucia Martins Diniz
Emilly Neves Souza
Luana Amaral de Moura
Marcela Scárdua Sabbagh de Azevedo

DOI:

https://doi.org/10.47456/rbps.v25i2.41037

Keywords:

Adult-onset scleredema, Diabetes Mellitus, Paraproteinemias

Abstract

Introduction: Scleredema of Buschke (SB) is a rare condition characterized by thickening and hardening of the skin, primarily affecting the neck, shoulders, and upper back. It is associated with diabetes mellitus, monoclonal gammopathy, infections, and other factors. It can cause limited mobility and discomfort. Diagnosis can be challenging, with prognosis linked to early detection. Case reports: We report two cases of SB associated with monoclonal gammopathy and diabetes mellitus, highlighting its relationship with various etiologies. Conclusion: The reported cases were diagnosed with SB, with case 1 involving a patient with diabetes and monoclonal gammopathy, classified as subtype 2, and case 2 related to poorly controlled glucose levels in the context of type 2 diabetes, classified as subtype 3. Both cases are undergoing variable treatment, experiencing periods of improvement, stabilization, and exacerbation.

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