Case report of scleredema of Buschke with monoclonal gammopathy and type 2 diabetes mellitus

Authors

  • Alexandre Calegari Oliosi Hospital Universitário Cassiano Antonio Moraes - Hucam/Ufes https://orcid.org/0000-0001-6191-631X
  • Lucia Martins Diniz
  • Emilly Neves Souza
  • Luana Amaral de Moura
  • Marcela Scárdua Sabbagh de Azevedo

DOI:

https://doi.org/10.47456/rbps.v25i2.41037

Keywords:

Adult-onset scleredema, Diabetes Mellitus, Paraproteinemias

Abstract

Introduction: Scleredema of Buschke (SB) is a rare condition characterized by thickening and hardening of the skin, primarily affecting the neck, shoulders, and upper back. It is associated with diabetes mellitus, mono­clonal gammopathy, infections, and other factors. It can cause limited mobility and discomfort. Diagnosis can be challenging, with prognosis linked to early detection. Case reports: We report two cases of SB associat­ed with monoclonal gammopathy and diabetes mellitus, highlighting its relationship with various etiologies. Conclusion: The reported cases were diagnosed with SB, with case 1 involving a patient with diabetes and monoclonal gammopathy, classified as subtype 2, and case 2 related to poorly controlled glucose levels in the context of type 2 diabetes, classified as subtype 3. Both cases are undergoing variable treatment, experiencing periods of improvement, stabilization, and exacerbation.

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References

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Published

2023-11-06

How to Cite

1.
Calegari Oliosi A, Martins Diniz L, Neves Souza E, Amaral de Moura L, Scárdua Sabbagh de Azevedo M. Case report of scleredema of Buschke with monoclonal gammopathy and type 2 diabetes mellitus. RBPS [Internet]. 2023 Nov. 6 [cited 2025 Jun. 6];25(4):44-8. Available from: https://periodicos.ufes.br/rbps/article/view/41037

Issue

Vol. 25 No. 4 (2023)

Section

Relato de Caso

License

Copyright (c) 2023 Brazilian Journal of Health Research

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